We report a case of adult-onset congenital hepatic fibrosis (CHF). The patient, who was a woman in her twenties, presented pancytopenia. Abdominal CT and MRI show mild dilation of intrahepatic bile duct, multiple renal cysts, and portal hypertension, such as splenomegaly, hepatic deformity, collateral vessels. CHF is an inherited disorder that belongs to the family of ductal plate malformation. CHF is rare disease, but we should know imaging findings of this.
|Number of pages
|Japanese Journal of Clinical Radiology
|Published - 2011 Sept 10
ASJC Scopus subject areas
- Radiology Nuclear Medicine and imaging