A case of adult-onset congenital hepatic fibrosis

T. Nozaki, N. Muraishi, S. Fuwa, Y. Onoda, M. Kamo, Y. Okajima, Y. Saida, K. Suzuki

Research output: Contribution to journalArticlepeer-review


We report a case of adult-onset congenital hepatic fibrosis (CHF). The patient, who was a woman in her twenties, presented pancytopenia. Abdominal CT and MRI show mild dilation of intrahepatic bile duct, multiple renal cysts, and portal hypertension, such as splenomegaly, hepatic deformity, collateral vessels. CHF is an inherited disorder that belongs to the family of ductal plate malformation. CHF is rare disease, but we should know imaging findings of this.

Original languageEnglish
Pages (from-to)1108-1111
Number of pages4
JournalJapanese Journal of Clinical Radiology
Issue number9
Publication statusPublished - 2011 Sept 10
Externally publishedYes

ASJC Scopus subject areas

  • Radiology Nuclear Medicine and imaging


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