Infantile congenital petrosal cholesteatoma: A case report and literature review

Kazuharu Yamazaki, Hiroaki Sato, Kazuo Murai, Kaoru Ogawa

Research output: Contribution to journalArticlepeer-review

3 Citations (Scopus)


Congenital cholesteatoma of the middle ear is frequently seen in younger children including infant. By contrast, that of the petrous bone is rarely seen in younger children. We report an exceptional case occurring in 23-month-old infant who presented with unilateral facial nerve paralysis at about 18-month-old. Computed tomography and magnetic resonance imaging revealed congenital cholesteatoma measuring approximately 2 cm in the area of the right geniculate ganglion. The mass was completely eradicated via the middle fossa approach, which allowed for preservation of hearing. The facial nerve maintained intact during surgery and paralysis showed partial recovery after the operation. To our knowledge, the present case seems to be the youngest case of congenital petrosal cholesteatoma reported, and also demonstrates congenital petrosal cholesteatoma could exhibit facial nerve paralysis in early childhood.

Original languageEnglish
Pages (from-to)1703-1707
Number of pages5
JournalInternational Journal of Pediatric Otorhinolaryngology
Issue number12
Publication statusPublished - 2005 Dec
Externally publishedYes


  • Congenital petrosal cholesteatoma
  • Facial nerve paralysis
  • Infant

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Otorhinolaryngology


Dive into the research topics of 'Infantile congenital petrosal cholesteatoma: A case report and literature review'. Together they form a unique fingerprint.

Cite this