Stepwise Total Aortic Repairs With Fenestrated Endografts in a Patient With Loeys-Dietz Syndrome

Kenichi Hashizume; Hideyuki Shimizu; Masanori Honda; Shinya Inoue; Hidenobu Takaki; Kanako Hayashi; Hiroaki Kaneyama

doi:10.1016/j.athoracsur.2017.02.017

Stepwise Total Aortic Repairs With Fenestrated Endografts in a Patient With Loeys-Dietz Syndrome

Kenichi Hashizume, Hideyuki Shimizu, Masanori Honda, Shinya Inoue, Hidenobu Takaki, Kanako Hayashi, Hiroaki Kaneyama

Research output: Contribution to journal › Article › peer-review

6 Citations (Scopus)

Abstract

Loeys-Dietz syndrome (LDS) is a rare connective tissue disorder (CTD) caused by mutations in the gene encoding transforming growth factor-β receptors Ⅰ and Ⅱ. Patients with LDS manifest spontaneous aneurysms and dissections of the aorta and peripheral artery. We report a successful treatment with a hybrid endovascular repair for a rapidly expanding thoracoabdominal aneurysm in a 41-year-old woman affected by LDS. To overcome the difficulties of anatomical and surgical repair, we applied an original strategy using surgeon-modified fenestrated endografts.

Original language	English
Pages (from-to)	e39-e42
Journal	Annals of Thoracic Surgery
Volume	104
Issue number	1
DOIs	https://doi.org/10.1016/j.athoracsur.2017.02.017
Publication status	Published - 2017 Jul

ASJC Scopus subject areas

Surgery
Pulmonary and Respiratory Medicine
Cardiology and Cardiovascular Medicine

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title = "Stepwise Total Aortic Repairs With Fenestrated Endografts in a Patient With Loeys-Dietz Syndrome",

abstract = "Loeys-Dietz syndrome (LDS) is a rare connective tissue disorder (CTD) caused by mutations in the gene encoding transforming growth factor-β receptors Ⅰ and Ⅱ. Patients with LDS manifest spontaneous aneurysms and dissections of the aorta and peripheral artery. We report a successful treatment with a hybrid endovascular repair for a rapidly expanding thoracoabdominal aneurysm in a 41-year-old woman affected by LDS. To overcome the difficulties of anatomical and surgical repair, we applied an original strategy using surgeon-modified fenestrated endografts.",

author = "Kenichi Hashizume and Hideyuki Shimizu and Masanori Honda and Shinya Inoue and Hidenobu Takaki and Kanako Hayashi and Hiroaki Kaneyama",

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AU - Hashizume, Kenichi

AU - Shimizu, Hideyuki

AU - Honda, Masanori

AU - Inoue, Shinya

AU - Takaki, Hidenobu

AU - Hayashi, Kanako

AU - Kaneyama, Hiroaki

PY - 2017/7

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AB - Loeys-Dietz syndrome (LDS) is a rare connective tissue disorder (CTD) caused by mutations in the gene encoding transforming growth factor-β receptors Ⅰ and Ⅱ. Patients with LDS manifest spontaneous aneurysms and dissections of the aorta and peripheral artery. We report a successful treatment with a hybrid endovascular repair for a rapidly expanding thoracoabdominal aneurysm in a 41-year-old woman affected by LDS. To overcome the difficulties of anatomical and surgical repair, we applied an original strategy using surgeon-modified fenestrated endografts.

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Stepwise Total Aortic Repairs With Fenestrated Endografts in a Patient With Loeys-Dietz Syndrome

Abstract

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