TY - JOUR
T1 - A case of adult-onset congenital hepatic fibrosis
AU - Nozaki, T.
AU - Muraishi, N.
AU - Fuwa, S.
AU - Onoda, Y.
AU - Kamo, M.
AU - Okajima, Y.
AU - Saida, Y.
AU - Suzuki, K.
PY - 2011/9/10
Y1 - 2011/9/10
N2 - We report a case of adult-onset congenital hepatic fibrosis (CHF). The patient, who was a woman in her twenties, presented pancytopenia. Abdominal CT and MRI show mild dilation of intrahepatic bile duct, multiple renal cysts, and portal hypertension, such as splenomegaly, hepatic deformity, collateral vessels. CHF is an inherited disorder that belongs to the family of ductal plate malformation. CHF is rare disease, but we should know imaging findings of this.
AB - We report a case of adult-onset congenital hepatic fibrosis (CHF). The patient, who was a woman in her twenties, presented pancytopenia. Abdominal CT and MRI show mild dilation of intrahepatic bile duct, multiple renal cysts, and portal hypertension, such as splenomegaly, hepatic deformity, collateral vessels. CHF is an inherited disorder that belongs to the family of ductal plate malformation. CHF is rare disease, but we should know imaging findings of this.
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M3 - Article
AN - SCOPUS:80053538968
SN - 0009-9252
VL - 56
SP - 1108
EP - 1111
JO - Japanese Journal of Clinical Radiology
JF - Japanese Journal of Clinical Radiology
IS - 9
ER -