TY - JOUR
T1 - Aortic carboxypeptidase-like protein, a WNT ligand, exacerbates nonalcoholic steatohepatitis
AU - Teratani, Toshiaki
AU - Tomita, Kengo
AU - Suzuki, Takahiro
AU - Furuhashi, Hirotaka
AU - Irie, Rie
AU - Nishikawa, Makoto
AU - Yamamoto, Junji
AU - Hibi, Toshifumi
AU - Miura, Soichiro
AU - Minamino, Tohru
AU - Oike, Yuichi
AU - Hokari, Ryota
AU - Kanai, Takanori
N1 - Funding Information:
The authors thank Henry M. Kronenberg (Massachusetts General Hospital and Harvard Medical School) for the generous gift of collagen 1α1 promoter-DKK-1 Tg mice, and Makoto Seo (Saitama Medical University) for the generous gift of an expression vector with a luciferase gene downstream of the human PPARγ promoter. The authors also thank Akira Kikuchi (Osaka University) for helpful discussion and critical comments. This study was supported in part by a Grant-in-Aid for Scientific Research from the Ministry of Education, Culture, Sports, Science, and Technology of Japan (to KT).
Publisher Copyright:
© 2018 American Society for Clinical Investigation. All rights reserved.
PY - 2018/4/2
Y1 - 2018/4/2
N2 - Incidence of nonalcoholic steatohepatitis (NASH), which is considered a hepatic manifestation of metabolic syndrome, has been increasing worldwide with the rise in obesity; however, its pathological mechanism is poorly understood. Here, we demonstrate that the hepatic expression of aortic carboxypeptidase-like protein (ACLP), a glycosylated, secreted protein, increases in NASH in humans and mice. Furthermore, we elucidate that ACLP is a ligand, unrelated to WNT proteins, that activates the canonical WNT pathway and exacerbates NASH pathology. In the liver, ACLP is specifically expressed in hepatic stellate cells (HSCs). As fatty liver disease progresses, ACLP expression is enhanced via activation of STAT3 signaling by obesity-related factors in serum. ACLP specifically binds to frizzled-8 and low-density lipoprotein-related receptor 6 to form a ternary complex that activates canonical WNT signaling. Consequently, ACLP activates HSCs by inhibiting PPARγ signals. HSC-specific ACLP deficiency inhibits fibrosis progression in NASH by inhibiting canonical WNT signaling in HSCs. The present study elucidates the role of canonical WNT pathway activation by ACLP in NASH pathology, indicating that NASH can be treated by targeting ACLP-induced canonical WNT pathway activation in HSCs.
AB - Incidence of nonalcoholic steatohepatitis (NASH), which is considered a hepatic manifestation of metabolic syndrome, has been increasing worldwide with the rise in obesity; however, its pathological mechanism is poorly understood. Here, we demonstrate that the hepatic expression of aortic carboxypeptidase-like protein (ACLP), a glycosylated, secreted protein, increases in NASH in humans and mice. Furthermore, we elucidate that ACLP is a ligand, unrelated to WNT proteins, that activates the canonical WNT pathway and exacerbates NASH pathology. In the liver, ACLP is specifically expressed in hepatic stellate cells (HSCs). As fatty liver disease progresses, ACLP expression is enhanced via activation of STAT3 signaling by obesity-related factors in serum. ACLP specifically binds to frizzled-8 and low-density lipoprotein-related receptor 6 to form a ternary complex that activates canonical WNT signaling. Consequently, ACLP activates HSCs by inhibiting PPARγ signals. HSC-specific ACLP deficiency inhibits fibrosis progression in NASH by inhibiting canonical WNT signaling in HSCs. The present study elucidates the role of canonical WNT pathway activation by ACLP in NASH pathology, indicating that NASH can be treated by targeting ACLP-induced canonical WNT pathway activation in HSCs.
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U2 - 10.1172/JCI92863
DO - 10.1172/JCI92863
M3 - Article
C2 - 29553485
AN - SCOPUS:85045061318
SN - 0021-9738
VL - 128
SP - 1581
EP - 1596
JO - Journal of Clinical Investigation
JF - Journal of Clinical Investigation
IS - 4
ER -