Stepwise Total Aortic Repairs With Fenestrated Endografts in a Patient With Loeys-Dietz Syndrome

Kenichi Hashizume; Hideyuki Shimizu; Masanori Honda; Shinya Inoue; Hidenobu Takaki; Kanako Hayashi; Hiroaki Kaneyama

doi:10.1016/j.athoracsur.2017.02.017

Stepwise Total Aortic Repairs With Fenestrated Endografts in a Patient With Loeys-Dietz Syndrome

Kenichi Hashizume, Hideyuki Shimizu, Masanori Honda, Shinya Inoue, Hidenobu Takaki, Kanako Hayashi, Hiroaki Kaneyama

研究成果: Article › 査読

6 被引用数 (Scopus)

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Loeys-Dietz syndrome (LDS) is a rare connective tissue disorder (CTD) caused by mutations in the gene encoding transforming growth factor-β receptors Ⅰ and Ⅱ. Patients with LDS manifest spontaneous aneurysms and dissections of the aorta and peripheral artery. We report a successful treatment with a hybrid endovascular repair for a rapidly expanding thoracoabdominal aneurysm in a 41-year-old woman affected by LDS. To overcome the difficulties of anatomical and surgical repair, we applied an original strategy using surgeon-modified fenestrated endografts.

本文言語	English
ページ（範囲）	e39-e42
ジャーナル	Annals of Thoracic Surgery
巻	104
号	1
DOI	https://doi.org/10.1016/j.athoracsur.2017.02.017
出版ステータス	Published - 2017 7月

ASJC Scopus subject areas

外科
呼吸器内科
循環器および心血管医学

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10.1016/j.athoracsur.2017.02.017

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abstract = "Loeys-Dietz syndrome (LDS) is a rare connective tissue disorder (CTD) caused by mutations in the gene encoding transforming growth factor-β receptors Ⅰ and Ⅱ. Patients with LDS manifest spontaneous aneurysms and dissections of the aorta and peripheral artery. We report a successful treatment with a hybrid endovascular repair for a rapidly expanding thoracoabdominal aneurysm in a 41-year-old woman affected by LDS. To overcome the difficulties of anatomical and surgical repair, we applied an original strategy using surgeon-modified fenestrated endografts.",

author = "Kenichi Hashizume and Hideyuki Shimizu and Masanori Honda and Shinya Inoue and Hidenobu Takaki and Kanako Hayashi and Hiroaki Kaneyama",

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AU - Hashizume, Kenichi

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AU - Honda, Masanori

AU - Inoue, Shinya

AU - Takaki, Hidenobu

AU - Hayashi, Kanako

AU - Kaneyama, Hiroaki

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AB - Loeys-Dietz syndrome (LDS) is a rare connective tissue disorder (CTD) caused by mutations in the gene encoding transforming growth factor-β receptors Ⅰ and Ⅱ. Patients with LDS manifest spontaneous aneurysms and dissections of the aorta and peripheral artery. We report a successful treatment with a hybrid endovascular repair for a rapidly expanding thoracoabdominal aneurysm in a 41-year-old woman affected by LDS. To overcome the difficulties of anatomical and surgical repair, we applied an original strategy using surgeon-modified fenestrated endografts.

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Stepwise Total Aortic Repairs With Fenestrated Endografts in a Patient With Loeys-Dietz Syndrome

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